What is congenital lobar emphysema?
What is congenital lobar emphysema?
Congenital lobar emphysema (CLE), also known as congenital alveolar overdistension, is a developmental anomaly of the lower respiratory tract that is characterized by hyperinflation of one or more of the pulmonary lobes [1,2].
How is congenital lobar emphysema diagnosed?
Congenital lobar emphysema is a rare developmental anomaly of lungs that occurs mostly due to defective bronchial cartilages. It is diagnosed with a chest x-ray or ct-scan and treated with lobectomy in severe symptomatic cases.
What is congenital COPD?
Congenital lobar emphysema (CLE), also called congenital lobar overinflation (CLO), is a rare anomaly of fetal lung development in which an obstruction of the airways leads to an enlarged, overinflated lobe or lobes of the lung.
What causes infant emphysema?
What causes pulmonary interstitial emphysema? PIE most often happens in preterm infants. It occurs when their lungs don’t make enough of a substance called surfactant. Surfactant allows alveoli to be more flexible and less likely to break open.
How is congenital lobar emphysema treated?
However, if the condition seriously affects the patient’s ability to breathe, the usual treatment is the surgical removal (resection) of the affected lobe of the lung or the whole lung on the affected side.
What are the complications of emphysema?
Complications of emphysema can include: pneumonia – this is an infection of the alveoli and bronchioles. People with emphysema are more prone to pneumonia. collapsed lung – some lungs develop large air pockets (bullae), which may burst, resulting in lung deflation (also called pneumothorax)
Can a child be born with emphysema?
Emphysema occurs when there is damage to the alveoli (air sacs in the lungs). Typically a characteristic of adults with a history of smoking, this lung condition causes severe shortness of breath. In very rare cases, children can develop emphysema due to an abnormality that is present when they are born.
What are the different stages of emphysema?
Stage 1 or Mild (80% of normal) Stage 2 or Moderate (50-80%) Stage 3 or Severe (30-50%) emphysema. Stage 4 or Very severe, (less than 30%), end-stage, severe or end-stage emphysema.
