How rare is a Quadricuspid aortic valve?

How rare is a Quadricuspid aortic valve?

Quadricuspid aortic valve (QAV) is a rare congenital anomaly with an incidence of 0.01–0.04%.

How many people have a Quadricuspid aortic valve?

Quadricuspid aortic valves are very rare cardiac valvular anomalies with a prevalence of 0.013% to 0.043% of cardiac cases and a prevalence of 1 in 6000 patients that undertake aortic valve surgery.

How rare is a Unicuspid aortic valve?

Unicuspid aortic valve is an extremely rare congenital malformation, first reported by Edwards in 1958. The annual incidence of UAV has been estimated at 0.02% in the adult population. However, in those patients who undergo surgery for isolated aortic stenosis, it is encountered at a rate of 4% to 5%.

What is a Quadricuspid aortic valve?

Quadricuspid aortic valve (QAV) is a rare congenital cardiac defect characterized by the presence of four aortic valve leaflets of equal or varying sizes. Even rarer is its clinical presentation with aortic stenosis.

How common is Quadricuspid aortic valve?

Quadricuspid aortic valve (QAV) is a rare congenital heart disease with an incidence of 0.00028-0.00033% in autopsy series, 0.0059-0.0065% for patients undergoing transthoracic echocardiographic examinations and 0.05-1% for those receiving aortic valve replacements for aortic regurgitation (AR)[3,4].

What is Quadricuspid pulmonary valve?

The quadricuspid pulmonary valve is a rare congenital anomaly that can appear as an isolated morphologic variation or in the presence of other cardiac anomalies. Approximately 200 cases of quadricuspid pulmonary valves have been reported to date.

What is a Unicuspid aortic valve?

The unicuspid aortic valve is a very rare congenital anomaly, which usually presents as aortic stenosis, incompetence, or a combination of both. Other congenital disorders may accompany this phenomenon and aortic dilatation and left ventricular hypertrophy are frequent complications.

Is Unicuspid aortic valve genetic?

Although similar diseases (ie, bicuspids) have familial inheritance patterns, no familial UAV cases have been described. Contrary to this, our study demonstrated a family history of congenital aortic valve disease in 11% of patients with UAV, suggesting a possible genetic mechanism.

What is a Unicommissural valve?

Abstract. Background: Unicommissural aortic valves (UAVs) are rare anomalies in which adjacent cusps of two commissures are congenitally fused.

What is Unicuspid aortic valve?