Is fibrohistiocytic tumor cancer?
Is fibrohistiocytic tumor cancer?
Plexiform fibrohistiocytic tumor (PFT), a relatively newly described entity, is a soft tissue neoplasm of low malignant potential that most commonly affects children and young adults and only rarely occurs in the head and neck region.
What is fibrohistiocytic?
The fibrohistiocytic tumors of the skin are a heterogeneous group of dermal/subcutaneous mesenchymal neoplasms which show fibroblastic, myofibroblastic and histiocytic (macrophage-like) differentiation, often one beside the other in the same tumor.
What is a plexiform Fibrohistiocytic tumor?
Plexiform fibrohistiocytic tumor is a rare mesenchymal neoplasm of intermediate malignancy, first reported by Enzinger and Zhang in 1988. It has a predilection for children and young adults but can occur at any age. The tumor usually involves the upper limbs as a slow-growing, painless mass.
What is malignant fibrous histiocytoma?
Listen to pronunciation. (muh-LIG-nunt FY-brus HIS-tee-oh-sy-TOH-muh) A type of cancer that usually forms in the soft tissue, but it may also form in bone. It can occur anywhere in the body, but it usually occurs in the legs (especially the thighs), arms, or back of the abdomen.
What is an atypical Fibroxanthoma?
Atypical fibroxanthoma (AFX) is an uncommon, pleomorphic, spindle cell cutaneous malignancy that most commonly presents as a solitary red or pink papule or nodule on the head or neck (picture 1A) [1]. Exposure to ultraviolet light most likely contributes to the development of AFX.
Is atypical fibroxanthoma benign?
Atypical fibroxanthoma (AFX) is a recently described soft tissue tumour by World Health Organization as a benign tumour of uncertain differentiation, occurring on sun exposed skin in elderly individual [1].
How aggressive is atypical fibroxanthoma?
It is considered a superficial variant of undifferentiated pleomorphic sarcoma (formerly known as malignant fibrous histiocytoma). Although atypical fibroxanthoma has similar histologic features to undifferentiated pleomorphic sarcoma, it behaves less aggressively.
What is a plexiform tumor?
A tumor that forms in the tissue that covers and protects the nerves. Plexiform neurofibromas can occur anywhere in the body outside of the brain and spinal cord. They can occur on the face (including around the eye), neck, arms, legs, back, chest, abdomen, and internal organs.
What is plexiform schwannoma?
Plexiform schwannoma is a rare variant of Schwann cell tumor. Occurring in either conventional or cellular type, they are characterized either grossly or histologically by a plexiform pattern of intraneural growth often with multinodularity.
