What is a mesoblastic nephroma?

What is a mesoblastic nephroma?

Mesoblastic nephroma (also called fetal renal hamartoma) is the most common renal tumor identified in the neonatal period and the most frequent benign renal tumor in childhood. It represents 3-10% of all pediatric renal tumors. This tumor was first described as a separate entity by Bolande et al in 1967.

What causes Mesoblastic Nephroma?

Congenital mesoblastic nephroma is a rare renal tumor that is diagnosed during pregnancy and is associated with polyhydramnios, prematurity, and neonatal hypertension. Differential diagnoses include Wilms tumor, adrenal neuroblastoma, and other abdominal tumors.

Is congenital Mesoblastic Nephroma cancer?

Congenital mesoblastic nephroma (CMN) is a rare pediatric renal tumor with low malignant potential that most commonly occurs early in infancy.

What are Mesoblastic cells?

Abstract. Congenital mesoblastic nephroma (CMN) is a rare renal tumor of early infancy with a favorable outcome after complete surgical removal. CMN consists of a heterogeneous group of spindle cell tumors subdivided into “classical”, “cellular or atypical” and “mixed” forms based on histologic features.

What is the meaning of hepatoblastoma?

Hepatoblastoma is a rare tumor (an abnormal tissue growth) that originates in cells in the liver. It is the most common cancerous (malignant) liver tumor in early childhood.

What is Nephroblastomatosis?

Nephroblastomatosis is a rare preneoplastic lesion defined as the presence of diffuse or multifocal nephrogenic rests. They are divided into 4 categories: perilobar, intralobar, combined, and universal. The aim of this report is to describe a case of diffuse hyperplastic perilobar nephroblastomatosis.

What is clear cell sarcoma?

Clear cell sarcoma, or CCS, is a type of cancer called soft tissue sarcoma. CCS tumors occur most often in the arms, legs, feet, and hands. But, CCS can grow throughout the torso, including the stomach and intestines. CCS has also been found in the genitals and head.

What is the survival rate for hepatoblastoma?

Hepatoblastoma Prognosis Survival rates have reached 80-90 percent. This rate depends upon staging at diagnosis. Patients with fully resected tumors have a greater than 85 percent chance of survival. The rate is about 60 percent for those with metastatic disease that responds to chemo.

Can hepatoblastoma be cured?

The tumor can be cured with surgical removal. If surgical removal is hazardous because of size and location of this tumor inside the liver, cure is still possible with liver transplantation.

What is mesoblastic nephroma (CMN)?

Mesoblastic nephroma, also sometimes known as a congenital mesoblastic nephroma (CMN) or fetal renal hamartoma, is, in general, a benign renal tumor that typically occurs in utero or in infancy.

What does mesoblasti mean?

Mesoblastic nephromas are the most common renal tumors diagnosed in infancy, but may rarely also be encountered in older children.

What is axaxial CECT in nephroma?

Axial CECT in a patient with cellular mesoblastic nephroma shows a crescent of residual right kidney splayed along the posterior margin of the heterogeneous mass . This claw sign helps to identify the kidney as the organ of origin for the tumor.

What does longitudinal ultrasound of Nephroma of the lower kidney show?

Longitudinal ultrasound in a newborn shows a relatively small solid (but heterogeneous) mass involving only the lower pole of this kidney. The patient age, tumor size, & imaging features are typical for the classic type of mesoblastic nephroma.