What is congenital cystic Adenomatoid?
What is congenital cystic Adenomatoid?
Congenital cystic adenomatoid malformation (CCAM) is a benign lung lesion that appears before birth as a cyst or mass in the chest. It is made up of abnormal lung tissue that does not function properly, but continues to grow. CCAM is also frequently referred to as a congenital pulmonary airway malformation (CPAM).
What is the treatment of congenital cystic adenomatoid malformation?
Surgical intervention is the mainstay of therapy for CCAM including fetal surgery and postnatal surgical approaches. Fetal surgery should be considered in patients with large CCAMs and in cases complicated by hydrops, in which prognosis is poor.
What period of lung development will congenital cystic adenomatoid malformation develop?
It appears that the natural course of CCAM is growth until 25 weeks of gestation, after which it may plateau in size or even regress.
How is congenital cystic adenomatoid malformation diagnosed?
A congenital cystic adenomatoid malformation (CCAM) is usually diagnosed before birth during a pregnancy ultrasound, which will show a bright mass in the fetus’ chest. The size of the mass varies with each fetus and can change dramatically throughout the pregnancy.
How do you treat CPAM?
How is CPAM treated during pregnancy?
- Treatment with steroids to slow or stop the lesion’s growth.
- If there are large, fluid-filled cysts in your baby’s lungs, a doctor can drain them with a procedure called thoracentesis.
- Open fetal surgery to remove the lesion.
Can cystic adenomatoid malformation?
A congenital cystic adenomatoid malformation (CCAM) is an abnormality of one or more lobes in which the lobe forms as a fluid-filled sac, called a cyst, which does not function as normal lung tissue. CCAMs develop with equal frequency on either side of the lung, but rarely occur on both sides.
