What is the radiographic appearance of fibrous dysplasia?
The appearance of fibrous dysplasia is usually smooth and homogeneous with endosteal scalloping and cortical thinning 12. The borders are well defined and the cortex is usually intact but thinned due to the expansive nature of the lesion 12. Other features include: ground-glass matrix.
Is fibrous dysplasia hot on bone scan?
Like fibrous dysplasia, NOF is not associated with periosteal reaction and is not painful unless complicated by trauma. Bone scintigraphy may reveal increased uptake, ie, a “hot” appearance, during the “healing phase” of these lesions secondary to increased osteoblastic activity.
How is fibrous dysplasia diagnosed?
The primary tool for diagnosis of fibrous dysplasia is an X-ray. While bone appears solid in an X-ray, a fibrous dysplasia lesion has a relative distinct appearance often described as “ground glass.” The condition may be diagnosed, therefore, even in a person with no symptoms who is getting an X-ray for other reasons.
Is fibrous dysplasia an Expansile?
Fibrous dysplasia is thought to be particularly susceptible to bone cyst formation because of the vascularity of the lesion. Radiographically, the lesions appear as expansile cystic lesions with a bony shell, with either a fluid or soft tissue–appearing center.
What is shepherd crook deformity?
A shepherd crook deformity refers to a coxa varus angulation of the proximal femur, classically seen in femoral involvement by fibrous dysplasia, although may be seen in other disorders such as Paget disease of bone and osteogenesis imperfecta.
Is fibrous dysplasia treatable?
Although fibrous dysplasia is a genetic disorder, it’s caused by a gene mutation that’s not passed from parent to child. There’s no cure for the disorder. Treatment, which may include surgery, focuses on relieving pain and repairing or stabilizing bones.
Is fibrous dysplasia aggressive?
Although fibrous dysplasia (FD) is a benign fibro-osseous lesion, locally aggressive behaviour has rarely been described but is poorly characterised.